Craniocervical Instability in Ehlers-Danlos Syndrome Patients
The connection between Ehlers-Danlos Syndrome (EDS) and craniocervical instability is a relatively new concept and more research is needed. Some of the doctors “pioneering” in this connection are Dr. Paolo Bolognese and Dr. Fraser Henderson. More information on this topic will be posted shortly.
Canada “Based on our systematic review, we recommend that the CXA, Harris measurement (BDI & BAI), Grabb-Mapstone-Oakes measurement, and the angular displacement of C1 to C2 be used to evaluate suspected CCI in EDS patients. Surgical fixation of suspected CCI should only be performed in cases with clear radiographic presence of instability and concordant symptoms/signs. Consensus-based guidelines and care pathways are required.” Reference
UK “The clivo- axial angle measured in neutral was 139.7±10.4 degrees in the EDS group vs 148.9±8.4 in the control group (p<0.01) The cervical range of movement between flexion and extension was 74.6 (±24.4) in the EDS group vs. 39.4 (±11.3) in the controls (p<0.0001). Conclusion is EDS patients with neck symptoms exhibit different static as well as dynamic craniocervical structural features compared to a general population control. Reference